Long-term therapy of hereditary angioedema (HAE). Preventive management with fluoxymesterone and oxymetholone in severely affected males and females.
نویسندگان
چکیده
Le Petit and his associates (4) have reported a series of 86 cases in which they observed on the cathode ray screen pulsations which could be cinem~tographicalIy recorded. In our experience observation of the midline pulsations on the eRO is sometimes difficult because of rapid low amplitude fluctuations. The technique presented here makes possible the simultaneous presentation of electroencephalographic and echographic records, both of which are possible indicators of cerebral death.
منابع مشابه
Report on the First Survey of Iranian Patients with Hereditary Angioedema
Background: Hereditary angioedema (HAE) is a rare autosomal dominant primary immunodeficiency with complement system defect characterized by recurrent episodes of angioedema involving the skin or mucosa of the upper respiratory and gastrointestinal tracts. Objective: To characterize the clinical and laboratory data of hereditary angioedema in Iran. Methods: Patients with probable diagnosis of a...
متن کاملHereditary Angioedema in Swedish Adults: Report From the National Cohort.
Hereditary angioedema (HAE) is rare, disabling and sometimes life-threatening. The aim of this study is to describe its prevalence, symptomatology and treatment in Sweden. A total of 146 patients were identified; 110 adults and 36 children with HAE type I (n = 136) or II (n = 10), giving a minimal HAE prevalence of 1.54/100,000. All patients received a written questionnaire followed by a struct...
متن کاملSelf-administered C1 esterase inhibitor concentrates for the management of hereditary angioedema: usability and patient acceptance
Hereditary angioedema (HAE) is a rare genetic disease characterized by episodic subcutaneous or submucosal swelling. The primary cause for the most common form of HAE is a deficiency in functional C1 esterase inhibitor (C1-INH). The swelling caused by HAE can be painful, disfiguring, and life-threatening. It reduces daily function and compromises the quality of life of affected individuals and ...
متن کاملPerioperative care of a patient with hereditary angioedema
Hereditary angioedema is a rare disorder caused by the congenital deficiency or dysfunction of C1 inhibitor. The deficiency results in recurrent episodes of angioedema, mainly involving the mucosa and skin. The most common clinical manifestations are the result of edema in the subcutaneous tissue, abdominal mucosa, and laryngeal tissue. Laryngeal involvement remains the most serious due to the ...
متن کاملCase report: follow-up of long term prophylaxis of hereditary angioedema with an alternative attenuated androgenic drug
Background Hereditary Angioedema (HAE) is a disease caused by defective production or function of C1 inhibitor (C1INH) and transmitted by autossomic dominant inheritance pattern. Treatment of HAE is divided into three parts: short-term and long-term prophylaxis, and treatment of acute attacks. The long-term prophylaxis of HAE is aimed at reducing the frequency and severity of acute attacks. Thi...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید
ثبت ناماگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید
ورودعنوان ژورنال:
- The Johns Hopkins medical journal
دوره 135 6 شماره
صفحات -
تاریخ انتشار 1974